Síndrome de Still

Abstract

The present clinical case studied a 47- years old female patient with a pathological history of Systemic Lupus Erythematosus who suspended the usal medication, in addition to characteristic fascies was undergoing cardiogenetic study without chromosomal involvement was admitted by infectious respiratory condition accompanied by asthenia and poly arthralgia, for which recived treatment with antibiotics based on quinolones and analgesics that did not calm the pain; during her hospital stay present right hemiparesis of brachial predominance compatible with a picture of cerebrovascular disease and febrile peaks; immunological markers reported a deficiency of Protein C and S in addition to negative markers for Antiphospholipid Syndrome, which is suspected in Adult Still Disease. During hospitalization, the skin rash showed a reddish-colored maculopapular rash and was evaluated jointly with Dermatology and Medical Rheumatologists Staff of the “IESS Cuenca Hospital” that confirmed the diagnosis of Still syndrome given by Yamaguchi Criteria that gave a sensitivity of 92%; by the Biopsy of Injuries and Rheumatology got the diagnosis of Vasculitis plus Still Syndrome. At the moment patient who is being treated based on glucocorticoids plus immunosuppressants with marked clinical improvement so far.